{"id":24624,"date":"2021-05-24T00:02:01","date_gmt":"2021-05-23T23:02:01","guid":{"rendered":"https:\/\/radioljubuski.ba\/?p=24624"},"modified":"2021-05-24T00:02:02","modified_gmt":"2021-05-23T23:02:02","slug":"zivot-s-talasemijom-minor-rijec-strucnjaka","status":"publish","type":"post","link":"https:\/\/radioljubuski.ba\/index.php\/2021\/05\/24\/zivot-s-talasemijom-minor-rijec-strucnjaka\/","title":{"rendered":"\u017divot s talasemijom minor, rije\u010d stru\u010dnjaka"},"content":{"rendered":"\n<p class=\"wp-block-paragraph\"><strong>Talasemija minor u\u010destala je u mediteranskom podneblju. Rije\u010d je o autoimunoj nasljednoj bolesti koju karakterizira nedostatak hemoglobina, najva\u017enije karike u lancu prijenosa kisika. Otkrivamo kako se boriti protiv umora koji je jedan od glavnih uzroka talasemije.&nbsp;<\/strong><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">&#8211; Hemoglobin se sastoji od \u010detiri alfa lanca i dva beta lanca. Svaki od ovih lanaca ima svoj prijenosni gen i svaki od ovih lanaca, ukoliko do\u0111e do poreme\u0107aja u prijenosu, ima svoju klini\u010dku sliku, obja\u0161njava<strong>&nbsp;doc. Delfa Radi\u0107 Kri\u0161to<\/strong>, predstojnica Klinike za unutarnje bolesti KB Merkur.<br><br>Poreme\u0107aj mo\u017ee nastati na bilo kojem lancu hemoglobina, tako da govorimo o alfa ili beta talasemiji. Pacijenti koji imaju poreme\u0107aj u prijenosu samo jednog alfa lanca imaju ne\u0161to ni\u017ee vrijednosti hemoglobina i vode normalan \u017eivtot. Niti poreme\u0107aji na dva alfa lanca ne daju te\u017eu klini\u010dku sliku koja zahtijeva lije\u010denje.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">&#8211; Me\u0111utim kod talasemije alfa gdje imamo tri gena mutirana &#8211; to je ve\u0107 zna\u010dajan poreme\u0107aj koji zahtjeva puno br\u017eu obradu. Naj\u010de\u0161\u0107e se to detektira u djetinjstvu i kod malih pacijenata potrebna je vrlo ozbiljna terapija. Kad govorimo o \u010detvrtom tipu gdje su poreme\u0107ena genski sva \u010detiri alfa lanca &#8211; dolazi do intrauterine smrti, ili smrti bebe nakon poroda, dodaje doc. Radi\u0107 Kri\u0161to.<br><br><strong>Beta talasemija i razaranje crvenih krvnih zrnaca<\/strong><br><br>Kod beta talasemije mogu\u0107a su dva ishoda \u2013 bla\u017ei ili te\u017ei oblik, ovisno je li rije\u010d o poreme\u0107aju jednog ili oba beta lanca. Stoga je u dijagnosti\u010dkom smislu najva\u017enije odrediti o kojoj se podvrsti talasemije radi.<br><br>&#8211; Uobi\u010dajena analiza crvene krvne slike pokazuje pove\u0107ani broj crvenih krvnih zrnaca i ono \u0161to je vrlo bitno, ta crvena krvna zrnca su mala. Zna\u010di, gleda se prosje\u010dni volumen eritrocita koji je izrazito nizak i u krvnoj slici mo\u017eemo imati pove\u0107ani broj retikulocita. To je zato \u0161to je uz sve \u0161to se zbiva unutar organizma, nedostatak dijelova hemoglobina &#8211; prisutna uvijek i hemoliza (razaranje crvenih krvnih zrnaca), obja\u0161njava prof.<strong>&nbsp;Slobodanka Ostoji\u0107 Koloni\u0107<\/strong>, pro\u010delnica Zavoda za hematologiju KB Merkur.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Elektroforezom hemoglobina, kao zavr\u0161nom dijagnosti\u010dkom pretragom, odre\u0111uje se podvrsta talasemije \u2013 odnosno koji je lanac hemoglobina o\u0161te\u0107en. Na temelju dijagnosti\u010dkog nalaza, odre\u0111uje se i terapijski postupak. Lak\u0161i slu\u010dajevi obi\u010dno zahtijevaju samo kontinuirano pra\u0107enje krvne slike. Te\u017ee klini\u010dke slike daju izra\u017eenije simptome pa se one dijagnosticiraju jo\u0161 u dje\u010djoj dobi.<br><br><strong>Transplantacija ko\u0161tane sr\u017ei<\/strong><br><br>&#8211; \u0160to se ti\u010de terapije, glavni problem jest slabokrvnost i posljedice ni\u017ee vrijednosti hemoglobina na dje\u010dji organizam. Transfuzije crvenih krvnih zrnaca treba maksimalno izbjegavati, ali ih na\u017ealost ne mo\u017eemo izbje\u0107i. Zbog opetovanih transfuzija razvija se novo klini\u010dko stanje, jednako ozbiljno, a to je optere\u0107enje organizma \u017eeljezom, sa te\u0161kim o\u0161te\u0107enjem dva klju\u010dna organa &#8211; srca i jetre. Zato se kod najte\u017eih oblika talasemije planira i radi transplantacija ko\u0161tane sr\u017ei, dodaje prof. Ostoji\u0107 Koloni\u0107.<br><br>Blage klini\u010dke slike koje ne zahtijevaju lije\u010denje treba redovito kontrolirati, budu\u0107i da poreme\u0107aj u prijenosu kisika mo\u017ee utjecati na funkciju \u010ditavog organizma. Za kvalitetu \u017eivota bolesnika s talasemijom od iznimne su va\u017enosti zdrave \u017eivotne navike \u2013 pravilna prehrana i tjelesna aktivnost.<\/p>\n\n\n\n<div style=\"width: 640px;\" class=\"wp-video\"><video class=\"wp-video-shortcode\" id=\"video-24624-1\" width=\"640\" height=\"360\" preload=\"metadata\" controls=\"controls\"><source type=\"video\/mp4\" src=\"https:\/\/api.hrt.hr\/media\/4a\/40\/talasemija-hemoglobin-220521-20210522083748.mp4?_=1\" \/><a href=\"https:\/\/api.hrt.hr\/media\/4a\/40\/talasemija-hemoglobin-220521-20210522083748.mp4\">https:\/\/api.hrt.hr\/media\/4a\/40\/talasemija-hemoglobin-220521-20210522083748.mp4<\/a><\/video><\/div>\n\n\n\n<p class=\"wp-block-paragraph\">Izvor:hrt.hr<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Talasemija minor u\u010destala je u mediteranskom podneblju. Rije\u010d je o autoimunoj nasljednoj bolesti koju karakterizira nedostatak hemoglobina, najva\u017enije karike u lancu prijenosa kisika. Otkrivamo kako se boriti protiv umora koji je jedan od glavnih uzroka talasemije.&nbsp; &#8211; Hemoglobin se sastoji od \u010detiri alfa lanca i dva beta lanca. Svaki od ovih lanaca ima svoj prijenosni [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":24625,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1],"tags":[],"class_list":["post-24624","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-bihiregija"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.7 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>\u017divot s talasemijom minor, rije\u010d stru\u010dnjaka - RADIO LJUBU\u0160KI<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/radioljubuski.ba\/index.php\/2021\/05\/24\/zivot-s-talasemijom-minor-rijec-strucnjaka\/\" \/>\n<meta property=\"og:locale\" content=\"hr_HR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"\u017divot s talasemijom minor, rije\u010d stru\u010dnjaka - RADIO LJUBU\u0160KI\" \/>\n<meta property=\"og:description\" content=\"Talasemija minor u\u010destala je u mediteranskom podneblju. Rije\u010d je o autoimunoj nasljednoj bolesti koju karakterizira nedostatak hemoglobina, najva\u017enije karike u lancu prijenosa kisika. Otkrivamo kako se boriti protiv umora koji je jedan od glavnih uzroka talasemije.&nbsp; &#8211; Hemoglobin se sastoji od \u010detiri alfa lanca i dva beta lanca. 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